The left ventricular non compaction (LVNC) is a rare form of cardiomyopathy due to an abnormality in myocardial and endocardial embryogenesis in utero. We made a fortuitous diagnosis of this particular pathology using Doppler echocardiogram on a 58 year-old male patient. who presented with an ST elevation myocardial infarction. The treatment is based on symptomatic one. The prognosis seems to be unfortunate and the mortality rate is high based on the literature findings. This case is among rare cases found in the literature showing an association between LVNC and myocardial infarction with coronary artery disease.